Sézary Syndrome: A Crucial Cause of Uncontrollable Itching
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https://doi.org/10.60591/crspmi.181Keywords:
Lymphoma, T-Cell, Cutaneous; Mycosis Fungoides, Pruritus/etiology, Sezary Syndrome/complicationsAbstract
Erythroderma is a challenging condition characterized by
widespread erythema involving over 80% of the body surface, often with an unknown cause. Determining the etiology of erythroderma is a complex task due to its association with various pathologies. Sézary syndrome (SS), an aggressive leukemic variant of cutaneous T-cell lymphoma (CTCL), is one of the potential causes, leading to a traditionally poor short-term prognosis. Swift diagnosis is crucial as it significantly impacts the morbidity and mortality of these patients.
We present a clinical case of erythroderma associated with
SS, emphasizing the importance of early recognition and diagnosis of erythroderma associated with CTCL, since it has a significant impact on the morbidity and mortality of these patients.
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Copyright (c) 2024 Diana Isabel Rocha, Ana Novo, Sofia Moura Azevedo, Daniela Barroso
This work is licensed under a Creative Commons Attribution 4.0 International License.
