Kikuchi-Fujimoto Disease, a Rare Case of Lymphadenopaties
DOI:
https://doi.org/10.60591/crspmi.6Keywords:
Histiocytic Necrotizing Lymphadenitis, LymphadenopathyAbstract
Kikuchi-Fujimoto disease, or histiocytic necrotizing lymphadenitis, is a rare disease, of unknown cause. It is characterized by cervical lymphadenopathies and fever, and has usually a benign course. Its diagnosis is based on histopathologic examination, and it is important to distinguish from infectious and lymphoproliferative disorders that are clinically similar but with completely different treatment and prognosis. Besides that, it is important to be aware of its association with autoimmune diseases, namely systemic lupus erythematosus.
We report a clinical case of a young woman with fever and right supraclavicular lymphadenopathies, admitted with the suspicion of a lymphoproliferative syndrome, whose biopsy revealed this condition.
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