Bilateral Scleritis as a Presenting Manifestation of Relapsing Polychondritis
DOI:
https://doi.org/10.60591/crspmi.50Keywords:
Methotrexate, Polychondritis, Relapsing/diagnosis, Polychondritis, Relapsing/drug therapy, Scleritis/diagnosisAbstract
Relapsing polychondritis is a rare inflammatory condition with poorly understood physiopathology and unclear origin. It is commonly characterized by recurrent episodes of inflammation involving cartilaginous tissues, predominantly those of the ears, nose and joints. It may also have systemic manifestations, which can have potentially severe complications, such following respiratory tract involvement. Diagnosis is typically delayed, due to this vast clinical spectrum and there is no consensus on the ideal diagnostic approach or treatment choice.
We report the case of a patient presenting bilateral anterior nodular scleritis as the first manifestation of relapsing polychondritis. We attained disease control with methotrexate therapy, following recurrent disease upon tapering of high dose corticosteroids.
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