Sézary Syndrome: A Crucial Cause of Uncontrollable Itching

Authors

  • Diana Isabel Rocha Serviço de Medicina Interna, Unidade Local de Saúde Santo António, Porto, Portugal
  • Ana Novo Serviço de Medicina Interna, Unidade Local de Saúde Santo António, Porto, Portugal
  • Sofia Moura Azevedo Serviço de Medicina Interna, Unidade Local de Saúde Santo António, Porto, Portugal
  • Daniela Barroso Serviço de Medicina Interna, Unidade Local de Saúde Santo António, Porto, Portugal

DOI:

https://doi.org/10.60591/crspmi.181

Keywords:

Lymphoma, T-Cell, Cutaneous; Mycosis Fungoides, Pruritus/etiology, Sezary Syndrome/complications

Abstract

Erythroderma is a challenging condition characterized by
widespread erythema involving over 80% of the body surface, often with an unknown cause. Determining the etiology of erythroderma is a complex task due to its association with various pathologies. Sézary syndrome (SS), an aggressive leukemic variant of cutaneous T-cell lymphoma (CTCL), is one of the potential causes, leading to a traditionally poor short-term prognosis. Swift diagnosis is crucial as it significantly impacts the morbidity and mortality of these patients.

We present a clinical case of erythroderma associated with
SS, emphasizing the importance of early recognition and diagnosis of erythroderma associated with CTCL, since it has a significant impact on the morbidity and mortality of these patients.

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References

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Published

24-06-2024

How to Cite

Rocha, D. I., Novo, A., Moura Azevedo, S., & Barroso, D. (2024). Sézary Syndrome: A Crucial Cause of Uncontrollable Itching. SPMI Case Reports, 2(Edição Especial), 58–61. https://doi.org/10.60591/crspmi.181

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